netFormulary NHS
Milton Keynes Formulary
Milton Keynes University Hospital NHS Foundation Trust
Bedfordshire, Luton and Milton Keynes Clinical Commissioning Group
Milton Keynes Community Health Services
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 Formulary Chapter 9: Nutrition and blood - Full Chapter
09.08.01  Expand sub section  Drugs used in metabolic disorders
09.08.01  Expand sub section  Wilsons disease
Penicillamine
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Formulary
Red

Tablet 125mg 

 
   
Trientine
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Formulary
Red
NHS England
BlueTeq

Capsule 250mg, 300mg

 
Link  Clinical Commissioning Policy: Trientine for Wilson disease (all ages)
   
09.08.01  Expand sub section  Carnitine deficiency
Levocarnitine (Carnitor)
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Formulary
Red
High Cost Medicine
  • Oral liquid 100mg per 1ml = 1g/10ml, 10% solution
  • Oral liquid 300mg per 1ml = 1.5g/5ml, 30% Paediatric solution
  • Injection 200mg per 1ml = 1g in 5ml soultion
 
   
09.08.01  Expand sub section  Fabry's disease
09.08.01  Expand sub section  Gaucher's disease to top
09.08.01  Expand sub section  Mucopolysaccharidosis I
09.08.01  Expand sub section  Pompe disease
09.08.01  Expand sub section  Nephropathic cystinosis
Mercaptamine (Cystagon)
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Formulary
High Cost Medicine

Tablets 50mg

 
   
09.08.01  Expand sub section  Urea cycle disorders
 ....
 Non Formulary Items
Agalsidase Alfa and Beta  (Fabrazyme)

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Non Formulary
High Cost Medicine
 
Agalsidase Alfa and Beta  (Replagal)

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Non Formulary
High Cost Medicine
 
Alglucosidase Alfa  (Myozyme)

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Non Formulary
High Cost Medicine
 
Arginine

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Non Formulary
 
Asfotase alfa  (Strensiq)

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Non Formulary
High Cost Medicine
Link  NICE HST6: Asfotase alfa for treating paediatric-onset hypophosphatasia
 
Betaine
(Homocystinuria)

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Non Formulary
 
Biotin

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Non Formulary
 
Carglumic Acid  (Carbaglu)

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Non Formulary
High Cost Medicine
 
Chenodeoxycholic acid

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Non Formulary
Red Red
High Cost Medicine

This product must not be prescribed. Please contact Pharmacy for advice.

 
Chenodeoxycholic acid  (Leadiant biosciences)

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Non Formulary
Red Red
High Cost Medicine

This product must not be prescribed. Please contact Pharmacy for advice.

 
Eliglustat  (Cerdelga)

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Non Formulary
High Cost Medicine
Link  NICE HST5- Eliglustat for treating type 1 Gaucher disease
 
Elosulfase alfa  (Vimizim )

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Non Formulary
High Cost Medicine
Link  NICE HST2: Elosulfase alfa for treating mucopolysaccharidosis type IVa
 
Galsulfase  (Naglazyme)

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Non Formulary
 
Glycerol phenylbutyrate  (Ravicti)

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Non Formulary
NHS England
 
Imiglucerase  (Cerezyme)

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Non Formulary
High Cost Medicine
 
Laronidase  (Aldurazyme)

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Non Formulary
High Cost Medicine
 
Mercaptamine (cysteamine) eye drops

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Non Formulary
High Cost Medicine
 
Migalastat  (Galafold)

Non Formulary
High Cost Medicine
Link  NICE HST4: Migalastat for treating Fabry disease
 
Miglustat  (Zavesca)

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Non Formulary
High Cost Medicine
 
Nitisinone

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Non Formulary
 
Sebelipase alfa  (Kanuma)

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Non Formulary
 
Sodium Benzoate

Non Formulary
 
Sodium Dichloroacetate

Non Formulary
 
Sodium Phenylbutyrate

Non Formulary
 
Ubidecarenone

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Non Formulary
Link  DTB review of co-enzyme Q10 for statin related myopathy
 
Zinc Acetate  (Wilzin®)

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Non Formulary
 
  
Key
note Notes
Section Title Section Title (top level)
Section Title Section Title (sub level)
First Choice Item First Choice item
Non Formulary Item Non Formulary section
Restricted Drug
Restricted Drug
Unlicensed Drug
Unlicensed
Track Changes
Display tracking information
click to search medicines.org.uk
Link to adult BNF
click to search medicines.org.uk
Link to children's BNF
click to search medicines.org.uk
Link to SPCs
SMC
Scottish Medicines Consortium
Cytotoxic Drug
Cytotoxic Drug
CD
Controlled Drug
High Cost Medicine
High Cost Medicine
Cancer Drugs Fund
Cancer Drugs Fund
NHSE
NHS England
Homecare
Homecare
CCG
CCG

Traffic Light Status Information

Status Description

Green

Routine prescribing within licensed indication  

Amber 1

Specialist recommendation followed by GP initiation and continuation  

Amber 2

Specialist or GP initiation in line with local guideline after 1st line failure followed by GP continuation   

Amber 3

Specialist initiation and stabilisation followed by GP continuation  

Amber SCG

Specialist initiation and stabilisation followed by GP continuation in line with an agreed shared care guideline  

Red

Hospital or specialist prescribing only  

Red Red

These medicines have been evaluated and rejected by MKPAG and are NOT approved for use within MK. They are not recommended for use because of lack of clinical effectiveness, cost effectiveness or safety.  

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